EC31 Junctional epidermolysis bullosa
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01
Junctional (lucidolytic) epidermolysis bullosa is due to defects at the level of the lamina lucida of the epidermal basement membrane. The generalised severe form (Herlitz) is associated with widespread mucosal involvement of internal organs and has a high mortality in infancy.
synonyms
- Junctional epidermolysis bullosa
- Junctional EB - [epidermolysis bullosa]
- JEB - [junctional epidermolysis bullosa]
- Lucidolytic epidermolysis bullosa
- Junctional epidermolysis bullosa, generalised types
- Junctional epidermolysis bullosa, generalised severe
- Epidermolysis bullosa letalis
- Herlitz syndrome
- Herlitz junctional epidermolysis bullosa gravis
- JEB-H - [junctional epidermolysis bullosa, Herlitz]
- JEB-gen sev - [junctional epidermolysis bullosa, generalised severe]
- Junctional epidermolysis bullosa, generalised intermediate type
- GABEB - [generalised atrophic benign epidermolysis bullosa]
- JEB-nH gen - [junctional epidermolysis bullosa, non-Herlitz, generalised]
- JEB - [junctional epidermolysis bullosa] non-Herlitz, generalised
- generalised atrophic benign epidermolysis bullosa
- JEB-gen intermed - [junctional epidermolysis bullosa]
- Junctional epidermolysis bullosa with pyloric atresia
- JEB - [junctional epidermolysis bullosa] with pyloric atresia
- JEB-PA - [junctional epidermolysis bullosa with pyloric atresia]
- Junctional epidermolysis bullosa, late onset
- Epidermolysis bullosa progressiva
- JEB - [junctional epidermolysis bullosa] late onset
- JEB-LO - [junctional epidermolysis bullosa late onset]
- Junctional epidermolysis bullosa with respiratory and renal involvement
- Junctional epidermolysis bullosa, localised types
- Junctional epidermolysis bullosa, localised
- JEB-nH loc - [junctional epidermolysis bullosa, non-Herlitz, localised]
- JEB - [junctional epidermolysis bullosa] non-Herlitz, localised
- JEB-loc - [junctional epidermolysis bullosa, localised
- Junctional epidermolysis bullosa inversa
- JEB - [junctional epidermolysis bullosa] inversa
- JEB-inv - [junctional epidermolysis bullosa inversa]
- Junctional epidermolysis bullosa, LOC
- Laryngo-onycho-cutaneous syndrome
- Shabbir syndrome
- LOGIC
- JEB-LOC - [junctional epidermolysis bullosa laryngo-onycho-cutaneous] syndrome
- LOC - [laryngo-onycho-cutaneous] syndrome
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