5C64.20 Acrodermatitis enteropathica

International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01

Acrodermatitis enteropathica is an uncommon autosomal recessive disorder of intestinal zinc absorption. Signs usually appear within the first months of life with an exudative and crusted erythema located predominantly around body orifices (mouth, anogenital) and on the scalp and distal extremities. The signs are often misdiagnosed as being due to infection. The condition responds rapidly to zinc supplementation which must be continued throughout life.

synonyms

• Acrodermatitis enteropathica
• Danbolt-Closs syndrome
• Brandt syndrome
• primary zinc malabsorption syndrome

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