3A50.03 Homozygous or compound heterozygous alpha0 thalassaemia

International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01

Hb Bart's hydrops fetalis is the most severe form of alpha-thalassemia and is almost always lethal. It is characterised by fetal onset of generalised oedema, pleural and pericardial effusions, and severe hypochromic anaemia.

synonyms

• Homozygous or compound heterozygous alpha0 thalassaemia
• Hb Bart's hydrops fetalis
• Alpha thalassaemia hydrops fetalis
• Haemoglobin Bart hydrops fetalis

Thank you for choosing Find-A-Code, please Sign In to remove ads.