4A01.00 Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01
This refers to a hereditary type of primary immune deficiency disease characterised by a reduction in all types of gamma globulins, and rare X-linked genetic disorder that affects the body's ability to fight infection.
synonyms
- Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
- hereditary gamma globulin deficiency in blood
- hereditary agammaglobulinaemia antibody deficiency syndrome
- hereditary absence of gamma globulin in blood
- hereditary agammaglobulinaemia
- congenital sex-linked agammaglobulinaemia
- Isolated agammaglobulinaemia
- Autosomal recessive agammaglobulinaemia
- Agammaglobulinaemia, non-Bruton type
- Autosomal agammaglobulinaemia
- Swiss type autosomal recessive agammaglobulinaemia
- Swiss-type agammaglobulinaemia
- Ig beta deficiency
- Ig alpha deficiency
- Lambda 5 deficiency
- B-cell linker deficiency
- BLNK - [B-cell linker] deficiency
- X-linked agammaglobulinaemia
- Bruton agammaglobulinaemia
- Bruton type agammaglobulinaemia
- Bruton x-linked agammaglobulinaemia
- BTK - [Bruton tyrosine kinase] deficiency
- Bruton hypogammaglobulinaemia
- Syndromic agammaglobulinaemia
- Agammaglobulinaemia - microcephaly - craniosynostosis - severe dermatitis
- Immunodeficiency - centromeric region instability - facial anomalies syndrome
- Immunodeficiency - centromeric instability - facial anomalies
- Centromeric instability immunodeficiency syndrome
- Malignant myelodysplasia with hypogammaglobulinaemia
- Short stature due to growth hormone isolated deficiency with X-linked hypogammaglobulinaemia
- Hereditary hypogammaglobulinaemia antibody deficiency syndrome
- hereditary hypogammaglobulinaemia
- Severe combined immunodeficiency due to absent lymphoid stem cells
- SCID - [severe combined immunodeficiency] due to absent lymphoid stem cells
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