AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2022 Issue 4; New/Revised ICD-10-CM Codes

Activated Phosphoinositide 3-Kinase Delta Syndrome [APDS]

A new code was created to identify activated phosphoinositide 3-kinase delta syndrome (D81.82).APDS (PI3K delta syndrome) is a rare primary immune regulatory disorder (PIRD) caused by genetic variants in either one of two identified genes known as PIK3CD or PIK3R1. It is a combined immunodeficiency and impairs the immune system such that individuals with this condition typically have low numbers of white blood cells, particularly certain types of B cells and T cells.APDS usually manifests during early childhood. The most common symptoms are frequent and severe infections of the ears, sinuses, herpes virus infections, neurodevelopment delay...

To read the full article, sign in and subscribe to AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS .

Thank you for choosing Find-A-Code, please Sign In to remove ads.