Von Willebrand Disease

The provider documented the patient has both Von Willebrand disease (VWD), type 1, and Factor VIII (functional) deficiency. ICD-10-CM classifies VWD, type 1, to code D68.01 , Von Willebrand disease, type 1, and Factor VIII deficiency to code D66 , Heredity factor VIII deficiency. Codes D66 and D68.01 are mutually exclusive based on the Excludes1 notes located at both codes. What codes are assigned when both VWD type 1 and Factor VIII deficiency are documented? ...

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Note:  The following article synopsis was NOT provided by the AHA. It was created by Find-A-Code/innoviHealth.

Article Overview

This article reviews Von Willebrand disease as a coding and classification topic, with emphasis on ICD-10-CM code assignment by disease type. It is intended for medical coders, compliance staff, and other revenue cycle professionals who need a high-level understanding of how the condition is organized in the code set and how documentation may reflect different disease subtypes and related bleeding disorders.

Why This Topic Matters

Accurate classification of Von Willebrand disease affects diagnosis coding, documentation integrity, and claims processing when providers document specific subtypes or related coagulation conditions.

Article Sections

  1. ICD-10-CM code expansion for Von Willebrand disease

    This section introduces the updated ICD-10-CM classification for Von Willebrand disease and lists the subtype-based code structure.

  2. Overview of Von Willebrand disease and major types

    This section describes the condition in general and summarizes the main clinical types discussed in the article.

  3. Type 1, type 2, and type 3 characteristics

    This section outlines broad distinctions among the major disease types and their subtypes.

  4. Inheritance, symptoms, and acquired disease

    This section discusses general disease patterns, common signs, and the distinction between inherited and acquired forms.

  5. Documentation scenario and coding question

    This section presents a documentation scenario involving Von Willebrand disease and a related factor deficiency and frames a coding query about the diagnosis assignment.

What You Will Learn

  • How Von Willebrand disease is organized into ICD-10-CM categories
  • What broad clinical distinctions exist among the major disease types
  • How documentation may mention related coagulation deficiencies alongside Von Willebrand disease
  • What kind of coding issue arises when multiple related diagnoses are documented together

Who Should Read This

  • Medical coders
  • Coding auditors
  • Compliance professionals
  • Revenue cycle staff
  • Clinical documentation improvement specialists

Codes Discussed


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